Netherton syndrome-Ichthyosis linearis circumflexa-Bamboo hair = متلازمة نيثرتون

Netherton syndrome-Ichthyosis linearis circumflexa-Bamboo hair = متلازمة نيثرتون Netherton Syndrome Netherton syndrome is a rare, autosomal recessive disorder characterized by the concurrence of ichthyosis, a structural hair shaft abnormality, and atopy. The usual cutaneous manifestation is ichthyosis linearis circumflexa, a distinctive condition of generalized hyperkeratosis and polycyclic and serpiginous erythematous plaques with a characteristic, migratory, […]

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Neurofibroma =ورم ليفي عصبي

Neurofibroma =ورم ليفي عصبي   Neurofibroma   EPIDEMIOLOGY Neurofibromas often occur as solitary lesions and are common in the general population. NF1 has a prevalence of 1 in 4000.   ETIOLOGY AND PATHOGENESIS Neurofibromas are hyperplasias of all the nerves elements. Neurofibromas can be seen as sporadic lesions or in the context of NF1,. The […]

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